Open AccessParaneoplastic pemphigus and myasthenia gravis, associated with inflammatory pseudotumor‐like follicular dendritic cell sarcoma: response to rituximab
Author(s) -
Wang Lifang,
Deng Hui,
Mao Mei
Publication year - 2016
Publication title -
clinical case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.21
H-Index - 9
ISSN - 2050-0904
DOI - 10.1002/ccr3.625
Subject(s) - medicine , paraneoplastic pemphigus , rituximab , myasthenia gravis , pemphigus , pathology , autoimmune disease , sarcoma , lymphoproliferative disorders , inflammatory pseudotumor , immunology , disease , autoantibody , lymphoma , antibody , lesion
Key Clinical Message Paraneoplastic pemphigus ( PNP ) is an autoimmune blistering disease associated with neoplasms. The disease is most commonly of lymphoproliferative origin and presents high mortality. We describe a patient with PNP and myasthenia gravis associated with inflammatory pseudotumor‐like follicular dendritic cell sarcoma, as well as the response to rituximab.