Desmoplastic small round cell tumor: a case report

The desmoplastic small round cell tumor (DSRCT) is a neoplasm of rare occurrence, described in 1987 by Sesterhennet al. Currently, there are about 101 cases described in the consulted literature. The authors report a case of intra-abdominal DSRCT in a 53-year-old patient, carrier of a palpable mass in epigastrium, asymptomatic. The propaedeutics showed multiple expansive lesions of varying dimensions compromising the peritoneal cavity. The patient was referred to exploratory laparotomy; only cytoreductive surgery was possible. The intraoperative findings are described, tomographic, and macroscopic and immunohistochemical aspects. The patient was followed up at the Oncology Service. He died months after surgery.