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ABS TRACT Noonan syndrome (NS), is an autosomal dominant disorder commonly seen in child hood and is characterized by short stature, congenital heart defects and facial abnormalities (espe cially in adults) along with thoracic deformity. Lymphatic dysplasia can be seen with this syndrome causing chylothorax by development of fistulas between thoracic duct and pleural space or it can directly occur by malformation of thoracic lymphatic vessels. Hence, chylothorax can also be seen. Herein, we present a case with this syndrome and chylothorax secondary to possible lymphatic dysplasia. We achieved a great success with ocreotide and medium chain trigliserides in the man agement of chylothorax and hence suggest this therapy to other clinicians.

Successful Ocreotide and Medium-Chain Triglyceride Therapy for Cylothorax in a Patient with Noonan Syndrome: Case Report