Open AccessPulmonary Arterial Hypertension Combined with a High Cardiac Output State: Three Remarkable Cases
Author(s) -
Spruijt Onno A.,
Bogaard HarmJan,
VonkNoordegraaf Anton
Publication year - 2013
Publication title -
pulmonary circulation
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.791
H-Index - 40
ISSN - 2045-8940
DOI - 10.4103/2045-8932.113185
Subject(s) - medicine , pulmonary hypertension , cardiac catheterization , cardiac output , shunt (medical) , cardiology , right heart catheterization , hemodynamics
A congenital extrahepatic portosystemic venous shunt (CEPVS), also known as an Abernethy malformation, is a rare cause of pulmonary arterial hypertension (PAH). In this case series, we describe three male patients of 30, 23, and 27 years of age with PAH due to a CEPVS. In all three patients, a right heart catheterization revealed a high cardiac output. The aim of this case series is to make pulmonary hypertension physicians aware of the possibility of a CEPVS when PAH is accompanied with a high cardiac output state.