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Association of Cognitive and Behavioral Features Between Adults With Tuberous Sclerosis and Frontotemporal Dementia
Author(s) -
Andy Liu,
Adam M. Staffaroni,
Julio C. Rojas-Martinez,
Nicholas Olney,
Carolina Alquézar,
Peter A. Ljubenkov,
Renaud La Joie,
Jamie Fong,
Joanne Taylor,
Anna Karydas,
Eliana Marisa Ramos,
Giovanni Coppola,
Adam L. Boxer,
Gil D. Rabinovici,
Bruce L. Miller,
Aimee W. Kao
Publication year - 2019
Publication title -
jama neurology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 5.298
H-Index - 231
eISSN - 2168-6157
pISSN - 2168-6149
DOI - 10.1001/jamaneurol.2019.4284
Subject(s) - tuberous sclerosis , frontotemporal dementia , dementia , medicine , neuroimaging , psychology , pathology , psychiatry , disease
Individuals with tuberous sclerosis complex can develop a progressive neuropsychiatric syndrome known as tuberous sclerosis-associated neuropsychiatric disorders. Tuberous sclerosis-associated neuropsychiatric disorders symptoms overlap with clinical criteria for frontotemporal dementia, yet the association between the 2 has not been explored.

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