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Evaluation of Structural Progression in Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy
Author(s) -
Thomas P. Mast,
Cynthia A. James,
Hugh Calkins,
Arco J. Teske,
Crystal Tichnell,
Brittney Murray,
Peter Loh,
Stuart D. Russell,
Birgitta K. Velthuis,
Daniel P. Judge,
Dennis Dooijes,
Ryan J. Tedford,
Jeroen F. van der Heijden,
Harikrishna Tandri,
Richard N.W. Hauer,
Theodore P. Abraham,
Pieter A. Doevendans,
Anneline S.J.M. te Riele,
Maarten J. Cramer
Publication year - 2017
Publication title -
jama cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 6.108
H-Index - 63
eISSN - 2380-6591
pISSN - 2380-6583
DOI - 10.1001/jamacardio.2016.5034
Subject(s) - medicine , arrhythmogenic right ventricular dysplasia , cardiology , interquartile range , cardiomyopathy , ejection fraction , cohort , ventricular remodeling , heart failure
Considerable research has described the arrhythmic course of arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C). However, objective data characterizing structural progression, such as ventricular enlargement and cardiac dysfunction, in ARVD/C are relatively scarce.

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