Open AccessI-gel assisted fiberoptic intubation in a child with Morquio′s syndrome
Author(s) -
Sangeeta Dhanger,
S Adinarayanan,
Stalin Vinayagam,
Mohanasundaram Praveen Kumar
Publication year - 2015
Publication title -
saudi journal of anaesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.416
H-Index - 24
eISSN - 1658-354X
pISSN - 0975-3125
DOI - 10.4103/1658-354x.152893
Subject(s) - medicine , intubation , mucopolysaccharidosis , hunter syndrome , airway , anesthesia , endotracheal intubation , pediatrics , surgery
Morquio's syndrome, also known as mucopolysaccharidosis type IV is an autosomal recessive disorder, caused by deficiency of n-acetylgalactosamine-6-sulphate. Anesthetic management of this syndrome is a great challenge, especially in pediatric age group as "cannot ventilate, cannot intubate" scenario can be encountered by anesthesiologist due to the possibility of total airway collapse. Herewith, we are reporting a case of child with Morquio's syndrome where I-gel assisted fiber-optic intubation was used for safe endotracheal intubation.