Open AccessAtypical hemolytic uremic syndrome: A report of two cases
Author(s) -
Md. Habibur Rahman,
Mahmuda Akhter,
Syed Symul Haque
Publication year - 2016
Publication title -
bangabandhu sheikh mujib medical university journal
Language(s) - English
Resource type - Journals
eISSN - 2224-7750
pISSN - 2074-2908
DOI - 10.3329/bsmmuj.v9i1.28954
Subject(s) - medicine , fulminant , atypical hemolytic uremic syndrome , disease , pathogenesis , acute kidney injury , intensive care medicine , pediatrics , kidney disease , haemolytic uraemic syndrome , immunology , complement system , antibody , biochemistry , chemistry , escherichia coli , gene
Hemolytic uremic syndrome (HUS) is one of the important cause of acute kidney injury in children. There is excellent outcome in patients with typical HUS but atypical HUS is associated with high mortality, risk of recurrence and may lead to end stage renal disease. We report two cases of 5 and 6 year old child having clinical & laboratory characteristics of atypical HUS. These children had a fulminant course of illness with complications involving various systems. The report provides an insight into the etio pathogenesis, diagnoses and treatment of this condition