Open AccessNutritional Support for Child with Werdnig–Hoffmann Spinal Muscular Atrophy
Author(s) -
Е. А. Балакирева,
А. В. Слепухина,
П. В. Сериков,
О. А. Пученкова,
В. М. Михарева,
Ю. А. Багреева
Publication year - 2021
Publication title -
rossijskij vestnik perinatologii i pediatrii
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.139
H-Index - 4
eISSN - 2500-2228
pISSN - 1027-4065
DOI - 10.21508/1027-4065-2020-65-6-72-75
Subject(s) - medicine , spinal muscular atrophy , anthropometry , pediatrics , atrophy , perimeter , progressive muscular atrophy , disease , amyotrophic lateral sclerosis , geometry , mathematics
Some of the severe manifestations of Werdnig-Hoffmann disease are the pseudobulbar and bulbar syndromes complicated by the hypotrophy of the various degrees of severity. The clinical case of the nutritional support for the child with grade II hypotrophy that complicated the course of Werdnig–Hoffmann disease in one-year-old child is presented. The purpose of this study is to assess the effect of Clinutren Junior high-calorie formula for children from 1 to 10 years of age on the growth and development of the child diagnosed with type I spinal muscular atrophy. The results were analyzed according to the degree of change in the following anthropometric data: mid-arm circumference, mid-hip circumference, the size of the skin fold in the periumbilical region, as well as laboratory data, as follows: albumin, total protein, lymphocytes.