Open AccessUnilateral pleuroparenchymal fibroelastosis as a rare form of idiopathic interstitial pneumonia: A case report
Author(s) -
Jaeha Lee,
Hang-Jea Jang,
Jin Han Park,
Hyun-Kuk Kim,
Soo Kon Lee,
Jiyeon Kim,
Seongho Kim
Publication year - 2020
Publication title -
world journal of clinical cases
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.368
H-Index - 10
ISSN - 2307-8960
DOI - 10.12998/wjcc.v8.i18.4186
Subject(s) - medicine , interstitial lung disease , lung , usual interstitial pneumonia , pathology , fibrosis , lung biopsy , idiopathic pulmonary fibrosis , parenchyma , biopsy
Pleuroparenchymal fibroelastosis (PPFE) is a rare idiopathic interstitial pneumonia characterized by predominantly upper lobe involvement with pleural fibrosis and subjacent parenchymal fibrosis. Recently, there have been increasing reports of PPFE, and PPFE might coexist with other interstitial lung diseases in the lower lobe and upper lobe. However, cases of unilateral PPFE are scarce.