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Atypical pediatric presentation of lymphocytic thrombophilic arteritis: Diagnostic difficulties and recent nosological clarification
Author(s) -
JuanCarpena Gloria,
PalazónCabanes Juan Carlos,
SilvaOrtega Sandra,
BlanesMartínez Mar,
BetllochMás Isabel
Publication year - 2020
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/pde.14412
Subject(s) - medicine , arteritis , dermatology , presentation (obstetrics) , pathology , girl , surgery , psychology , developmental psychology
Abstract A 4‐year‐old girl presented with a 2‐month history of round, hypopigmented, slightly scaly patches measuring 1‐6 cm and encircled by an erythematous halo, first appearing on the lower limbs then spreading to the whole body. Three biopsies were taken as the condition progressed, each showing a lymphocytic infiltrate affecting a medium‐sized artery at the dermal‐subcutaneous junction, with a concentric fibrin ring. These findings are characteristic of lymphocytic thrombophilic arteritis (LTA). The young age of our patient and the type of skin lesions she developed make this an atypical presentation of LTA, which usually manifests as hyperpigmented macules on the lower extremities, predominantly in dark‐skinned women.