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Arrhythmogenic Right Ventricular Cardiomyopathy with Left Ventricular Involvement and Aortic Dissection
Author(s) -
MERTEN MICHAEL,
WILLEMS STEPHAN,
HEINEMANN AXEL,
MEINERTZ THOMAS
Publication year - 2004
Publication title -
pacing and clinical electrophysiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.686
H-Index - 101
eISSN - 1540-8159
pISSN - 0147-8389
DOI - 10.1111/j.1540-8159.2004.00453.x
Subject(s) - medicine , cardiology , ventricle , autopsy , aortic dissection , heart failure , dissection (medical) , cardiomyopathy , dilated cardiomyopathy , aorta , radiology
Ten years ago, a 59‐year‐old patient presented with ventricular fibrillations. The resting ECG showed findings typical for ARVC. Echocardiography and ventriculography confirmed the diagnosis of ARVC showing a dilated right ventricle with aneurysms. MRI showed additional fatty replacement of the LV. Furthermore, the diagnosis of a chronic aortic dissection was established. Two years after ICD implantation, the patient died of progressive right heart failure. On autopsy, most of the RV and parts of the LV were replaced by fatty tissue, and the media of the aorta showed degenerative changes. A pathogenetic link between the two diseases remains speculative at this time. (PACE 2004; 27:408–411)