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LINEAR SCLERODERMA IN CHILDREN
Author(s) -
EUBANKS LEIGH ELLEN,
McBURNEY ELIZABETH I.,
GALEN WESLEY,
REED RICHARD
Publication year - 1996
Publication title -
international journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.677
H-Index - 93
eISSN - 1365-4632
pISSN - 0011-9059
DOI - 10.1111/j.1365-4362.1996.tb03633.x
Subject(s) - medicine , etiology , scleroderma (fungus) , dermatology , pathogenesis , localized scleroderma , treatment modality , disease , surgery , pathology , lichen sclerosus , inoculation
Abstract Background. Linear scleroderma is a cutaneous disease of unknown etiology. It most often affects children, who develop band‐like lesions in an asymmetric distribution. The literature is reviewed as to the diagnosis, pathogenesis, and treatment of linear scleroderma. Case Report. Six new cases of linear scleroderma in children are reported. Their ages ranged from 6 to 17 years, and five were girls. A 17–year‐old girl had en coup de sabre. Multiple treatment modalities were used. All laboratory testing was negative. Conclusions. Linear scleroderma is a clinical diagnosis. The pathogenesis remains unknown. A consistently effective therapy has not been found, although diphenylhydantoin and ticlopidine hydrochloride should be evaluated in clinical trials.