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Diffuse Cutaneous Mastocytosis: Pseudoxanthomatous Variant
Author(s) -
Jain Rajesh,
Dogra Sunil,
Verma Shikha,
Mohanty Sambit K,
Handa Sanjeev
Publication year - 2002
Publication title -
the journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.9
H-Index - 65
eISSN - 1346-8138
pISSN - 0385-2407
DOI - 10.1111/j.1346-8138.2002.tb00280.x
Subject(s) - cutaneous mastocytosis , dermatology , medicine , pathology , systemic mastocytosis , skin lesion , urticaria pigmentosa , disease
Diffuse cutaneous mastocytosis is one of the extremely rare benign forms of mastocytosis that have varied clinical presentations. The pseudoxanthomatous variant is an extremely rare multinodular nonpigmented entity. Only two cases have been reported so far in the literature. We report a 21 year old female patient who had diffusely infiltrated skin with multiple papulo‐nodular lesions resembling xanthomas and the classical histopathological features of mastocytosis.