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Vulvar Cicatricial Pemphigoid of Childhood
Author(s) -
Schoeffler A.,
Roth B.,
Causeret A.,
Kanitakis J.,
Faure M.,
Claudy A.
Publication year - 2004
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.0736-8046.2004.21110.x
Subject(s) - medicine , cicatricial pemphigoid , dermatology , dapsone , pemphigoid , bullous pemphigoid , treatment modality , therapeutic modalities , surgery , immunology , antibody
Abstract: We report a 9‐year‐old girl with a vulvar autoimmune bullous dermatosis. A diagnosis of localized bullous pemphigoid or cicatricial pemphigoid was made on the basis of immunohistologic data. Since the lesions were unresponsive to topical corticosteroids but healed completely on dapsone at a dosage of 1.5 mg/kg/day, we favor the diagnosis of vulvar cicatricial pemphigoid. Only two such cases have been reported thus far. The diagnostic criteria and therapeutic modalities are discussed.