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Isolated peripheral pulmonary stenosis in Takayasu arteritis
Author(s) -
Alizadehasl Azin,
Saedi Sedigheh,
Ganji Hanifeh,
Pourafkari Leili
Publication year - 2020
Publication title -
international journal of rheumatic diseases
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.795
H-Index - 41
eISSN - 1756-185X
pISSN - 1756-1841
DOI - 10.1111/1756-185x.13742
Subject(s) - medicine , takayasu arteritis , peripheral , cardiology , stenosis , takayasu's arteritis , arteritis , vasculitis , disease
Takayasu arteritis is a chronic granulomatous vasculitis generally affecting large vessels including the thoracic aorta and its branches. Intimal proliferation subsequently causes segmental stenosis and occlusion, and frequently aneurysmal dilatation in the affected vessels. Although involvement of pulmonary arteries is not uncommon, isolated branch pulmonary stenosis is rarely encountered. Here, we report a patient presenting with isolated peripheral pulmonary stenosis as the primary manifestation of Takayasu arteritis.