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Plasma and erythrocyte fatty acid concentrations in long‐chain 3‐hydroxyacyl‐CoA dehydrogenase deficiency
Author(s) -
Lund A. M.,
Dixon M. A.,
Vreken P.,
Leonard J. V.,
Morris A. A. M.
Publication year - 2003
Publication title -
journal of inherited metabolic disease
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.462
H-Index - 102
eISSN - 1573-2665
pISSN - 0141-8955
DOI - 10.1023/a:1025175606891
Subject(s) - docosahexaenoic acid , medicine , endocrinology , dehydrogenase , fatty acid , long chain , biochemistry , chemistry , biology , enzyme , polyunsaturated fatty acid , polymer science
Plasma and erythrocyte fatty acids have been measured in 9 patients with long‐chain 3‐hydroxyacyl‐CoA dehydrogenase deficiency being treated with a low‐fat diet. No significant abnormality was detected and in particular docosahexaenoic acid was not deficient.