Open AccessIsolated Large Vessel Pulmonary Vasculitis as a Cause of Chronic Obstruction of the Pulmonary Arteries
Author(s) -
Hagan Guy,
Gopalan Deepa,
Church Colin,
Rassl Doris,
Mukhtyar Chetan,
Wistow Trevor,
Lang Chim,
Sivasothy Pasupathy,
Stewart Susan,
Jayne David,
Sheares Karen,
Tsui Steven,
Jenkins David P.,
PepkeZaba Joanna
Publication year - 2011
Publication title -
pulmonary circulation
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.791
H-Index - 40
ISSN - 2045-8940
DOI - 10.4103/2045-8932.87312
Subject(s) - medicine , vasculitis , pulmonary vasculature , chronic thromboembolic pulmonary hypertension , pulmonary hypertension , pulmonary artery , positron emission tomography , magnetic resonance imaging , radiology , pulmonary thromboendarterectomy , endarterectomy , cardiology , disease , stenosis
Isolated pulmonary artery involvement by large vessel vasculitis is rare. This case report describes two patients with large vessel pulmonary vasculitis initially thought to have chronic thromboembolic pulmonary hypertension who had their diagnosis revised following pulmonary endarterectomy surgery. Advances in imaging techniques such as positron emission tomography and magnetic resonance imaging have permitted complementary radiological methods of diagnosis and follow up of large vessel disease and these are discussed in conjunction with the immunosuppressive and operative management of these patients.